Monoclonal and Fibrillary Diseases
The Glomerular Center has actively investigated issues in the diagnosis and therapy of rare glomerular diseases related to abnormal bone marrow function. Recent publications
Nasr SH, Markowitz GS, Stokes MB, Seshan SV, Valderrama E, Appel GB, Aucouturier P, D'Agati VD. Proliferative glomerulonephritis with monoclonal IgG deposits: a distinct entity mimicking immune-complex glomerulonephritis. Kidney Int. Jan;65(1):85-96.2004
Rosenstock JL, Markowitz GS, Valeri AM, Sacchi G, Appel GB, D'Agati VD. Fibrillary and immunotactoid glomerulonephritis: Distinct entities with different clinical and pathologic features. Kidney Int. Apr;63(4):1450-61 2003.
Lin J, Markowitz GS, Valeri AM, Kambham N, Sherman WH, Appel GB, D'Agati VD.
Renal monoclonal immunoglobulin deposition disease: the disease spectrum. J Am Soc Nephrol. Jul;12(7):1482-92. 2001
Kambham N, Markowitz GS, Appel GB, Aucouturier P, D'Agati V. Heavy Chain Disease: The Disease Spectrum. AJKD 33:954-962,1999. |